Session 4: Hepatobiliary/Thoracic

Chairs: Naved Alizai, Leeds, UK & Mikko Pakarinen, Helsinki, Finland

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047 08.30-08.40 PROGNOSTICATORS OF BILIARY ATRESIA OUTCOMES IN THE NORDIC COUNTRIES – A MULTICENTER SURVEY OF I58 PATIENTS

Mikko Pakarinen1, Lars Søndergaard Johansen2, Jan Svensson3, Krsitin Bjørnland4, Vladimir Gatzinsky5, Pernilla Stenström6, Antti Koivusalo1, Jørgen Thorup2, Markus Almström3, Ragnhild Emblem4, Sigurdur Björnsson5, Torbjörn Backman6, Runal Almaas4, Hannu Jalanko1, Björn Fischler3, Nina Kvist21Children’s Hospital, University of Helsinki, Helsinki, Finland, 2Rigshospitalet, Copenhagen, Denmark, 3Astrid Lindgren Children´s Hospital, Karolinska University Hospital, Stockholm, Sweden, 4Oslo University Hospital and University of Oslo, Oslo, Norway, 5Queen Silvia Childrens Hospital, Gothenburg, Sweden, 6Skane University Hospital in Lund, Lund University, Lund, Sweden

048 08.40-08.45 EXAMINATION OF THE GALLBLADDER IN THE JAUNDICED NEONATE: A MISSED OPPORTUNITY TO DIAGNOSE BILIARY ATRESIA

Ayman Goneidy1, Evelyn Ong11Birmingham Children’s Hospital, Birmingham, UK

049 08.45-08.50 CORELLATING CLINICAL FINDINGS WITH  LIVER HISTOLOGY AT INITIAL PRESENTATION IN BILIARY ATRESIA

Priya Ramachandran1,2, Ashitha K.Unny1, Srinivas Sankaranarayanan1, Naresh Shanmugam2, Mukul Vij2, Mohamed Rela21K.K CHILDS Trust Hospital, CHILDS Trust Medical Research Foundation, Chennai, India, 2Gleneagles Global Hospital, National foundation for Liver Research, Chennai, India

050 08.50-08.55 SIGNIFICANCE AND MANAGEMENT OF BILE LAKES AFTER PORTOENTEROSTOMY FOR BILIARY ATRESIA

Daniel Ginström1,2, Antti Koivusalo1, Risto Rintala1, Mikko Pakarinen1,21Childrens’ Hospital, University of Helsinki, Helsinki, Finland, 2Pediatric Liver and Gut Research Group, University of Helsinki, Helsinki, Finland

051 08.55-09.00 CYTOKERATIN-20 EXPRESSION IN BILIARY ATRESIA: A POSSIBLE PROGNOSTIC MARKER

Enrico La Pergola1,2, Alberto Quaglia2, Mark Davenport11Dept: Paediatric Surgery, Kings College Hospital, LONDON, UK, 2Institute of Liver Studies, LONDON, UK

052 09.00-09.05 THE PLACENTA IN BILIARY ATRESIA: POINTERS TO AETIOLOGY?

Caroline Zabiejag Zwick1, Etienne Nel1, Pawel Schubert1, Samuel Moore11University of Stellenbosch, Cape Town, South Africa

053 09.05-09.15 PREMATURITY AND  BILIARY ATRESIA: DOES IT MATTER?

Natalie Durkin1, Katja Doerry1, Erica Makin1, Mark Davenport11Paediatric Surgery, Kings College Hospital, London, UK

054 09.15-09.20 OUTCOME FOR BILIARY ATRESIA PATIENTS IN A SMALL VOLUME CENTRE

Kristin Bjørnland1,2, Maren Hinna2, Ragnhild Emblem1,2, Gunnar Aksnes1, Kjetil Ertresvåg1, Kjetil Stensrud1, Ingegerd Aagenæs1, Anniken Østensen1, Truls Sanengen1, Pål Line1,2, Lars Aabakken1,2, Runar Almaas11Oslo University Hospital, Oslo, Norway, 2Oslo Universtiy, Oslo, Norway

055 09.20-09.25 LONG-TERM OUTCOMES AFTER KASAI PORTOENTEROSTOMY AT A LARGE REFERRAL CENTER

Pablo Laje1, Michael L Nance1, Ashley E Byrne1, Jessi Erlichman1, Kathleen M Loomes1, Elizabeth Rand1, Alan W Flake11The Children’s Hospital of Philadelphia, Philadelphia, PA, USA

056 09.25-09.30 DETERIORATION IN NATIVE LIVER FUNCTION IN LONG-TERM SURVIVORS OF PORTOENTEROSTOMY FOR BILIARY ATRESIA IS VIRTUALLY A DEATH SENTENCE IN JAPAN

Takanori Ochi1, Hiroki Nakamura1, Momoko Wada1, Tsuyoshi Tamura1, Tadaharu Okazaki1, Masahiko Urao1, Yoichi Ishizaki2, Seiji Kawasaki2, Mureo Kasahara3, Koichi Mizuta4, Geoffrey J. Lane1, Atsuyuki Yamataka11Department of Pediatric General and Urogenital Surgery, Juntendo University School of Medicine, Tokyo, Japan, 2Department of Hepatobiliary-Pancreatic Surgery, Juntendo University School of Medicine, Tokyo, Japan, 3Organ Transplantation Center, National Center for Child Health and Development, Tokyo, Japan, 4Transplant Surgery Division, Department of Surgery, Jichi Medical University, Tochigi, Japan

057 09.30-09.35 ABSENT INTRAHEPATIC PORTAL VEINS ARE ASSOCIATED WITH LIVER TUMOURS IN PATIENTS WITH CONGENITAL PORTOSYSTEMIC SHUNTS

Athanasios Tyraskis1, Annamaria Deangello2, Maria Sellars2, Claudio De Vito3, Richard Thompson3, Alberto Quaglia3, Nigel Heaton3, Mark Davenport11Paediatric Surgery, Kings College Hospital, London, UK, 2Radiology, Kings College Hospital, London, UK, 3Institute of Liver Studies, Kings College, London, UK

058 09.35-10.00 HOW ACCURATELY DOES BRONCHOSCOPY AT TIME OF INITIAL SURGERY PREDICT SYMPTOMATIC TRACHEOMALACIA IN OESOPHAGEAL ATRESIA/TRACHEO-OESOPHAGEAL FISTULA?

Hemanshoo Thakkar1, Manasvi Upadhyaya1, Iain Yardley11Evelina Children’s Hospital, Guy’s and St. Thomas’s NHS Foundation Trust, London, UK

059 09.40-09.45 CHEWING FUNCTION IN CHILDREN WITH REPAIRED ESOPHAGEAL ATRESIA-TRACHEOESOPHAGEAL FISTULA

Selen Serel Arslan1, Numan Demir1, Aynur Ayse Karaduman1, Feridun Cahit Tanyel2, Tutku Soyer21Hacettepe University Faculty of Health Sciences, Department of Physiotherapy and Rehabilitation, Ankara, Turkey, 2Hacettepe University Faculty of Medicine Department of Pediatric Surgery, Ankara, Turkey

060 09.45-09.50 ACELLULAR DIAPHRAGM-DERIVED EXTRACELLULAR MATRIX AS TISSUE SOBSTITUTE FOR CONGENITAL DIAPHRAGMATIC HERNIA REPAIR

Martina Piccoli1, Caterina Trevisan1,2, Arben Dedja3, Piero Pavan4, Chiara Franzin1, Luca Urbani5, Paolo De Coppi5, Michela Pozzobon11Fondazione Istituto di Ricerca Pediatrica Città della Speranza, Padova, Italy, 2Department of Women and Child health, University of Padova, Padova, Italy, 3Department of Cardiac, Thoracic and Vascular Sciences, University of Padova, Padova, Italy, 4Department of Industrial Engineering, University of Padova, Padova, Italy, 5UCL Institute of Child Health and Great Ormond Street Hospital, London, UK

061 09.50-09.55 EVALUATION OF DIAPHRAGMATIC ENGINEERING USING BIOSHEET, A COLLAGENOUS CONNECTIVE TISSUE MEMBRANE, TO REPAIR CONGENITAL DIAPHRAGMATIC HERNIA IN RABBIT

Keisuke Suzuki1, Makoto Komura1, Kan Terawaki1, Tetsuro Kodaka1, Takumi Gohara1, Hiroko Komura2, Yasuhide Nakayama31Department of Pediatric Surgery, Saitama Medical University, Iruma-gun/Saitama, Japan, 2Division of Tissue Engineering, Graduate School of Medicine, University of Tokyo, Bunkyo-ku/Tokyo, Japan, 3Division of Medical Engineering and Materials, National Cerebral and Cardiovascular Centre Research Institute, Suita-shi/Osaka, Japan

062 09.55-10.00 A QUARTER CENTURY RETROSPECTIVE REVIEW OF NEWBORN CDH ADMITTED TO A SINGLE ECMO CENTRE

Sandra Davis2, Mark Davis4, Morag Liddell1, Jonathan Coutts1, Gregor Walker1,3, Carl Davis1,31Royal Hospital for Children, Glasgow, UK, 2Queen Elizabeth University Hospital, Glasgow, UK, 3University of Glasgow, Glasgow, UK, 4Wishaw General Hospital, Lanarkshire, UK

063 10.00-10.05 RISK FACTORS ANALYSIS OF MORTALITY WITHIN 1 MONTH AFTER BIRTH IN CONGENITAL DIAPHRAGMATIC HERNIA

Chaeyoun Oh1, Joong Kee Youn1, Ji-Won Han1, Hee-Beom Yang1, Hyun-Young Kim1, Sung-Eun Jung11Seoul National University College of Medicine, Seoul, Republic of Korea

 

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